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Clinical Cardiovascular Research Center (CCRC)

URMC / Clinical Cardiovascular Research Center (CCRC) / LQTS Registry / LQTS Risk Score Calculator

LQTS Risk Score Calculator

This Long QT Syndrome Risk Calculator was developed for prediction of 5-year absolute risk of the first life-threatening arrhythmic event (defined as aborted cardiac arrest, sudden cardiac death, or appropriate implantable cardioverter defibrillator [ICD] shock) in LQTS patients, accounting for individual risk factors and their changes over time. The risk score was developed based on long-term follow-up data from the University of Rochester LQTS Registry in 1,509 LQTS patients with QTc of at least 470 ms regardless of genotype, and in 1,288 patients with single LQT, LQT2, or LQT3 gene mutation, regardless of QTc. The predictive models were externally validated in an independent cohort of 1,481 LQTS patients from Pavia, Italy.  Details of the study are available in the publication entitled: Assessment of Absolute Risk of Life-Threatening Cardiac Events in Long QT Syndrome Patients available at the Frontiers in Cardiovascular Medicine

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Date of Birth:


Gender:


QTc (in msec, Bazett's formula):


History of Syncope:


Genotype:


Patient will be continuously treated by beta blockers
Patient will not be treated by beta blockers

 
Prediction of 5-year absolute risk of the first life-threatening arrhythmic event (defined as aborted cardiac arrest, sudden cardiac death, or appropriate implantable cardioverter defibrillator [ICD] shock)


	


	

	
Disclaimer

	
This calculator should NOT be used in

	
· Patients with a previous history of cardiac arrest

	
· Patients who are genotype negative or with unknown genotype and has a QTc < 470ms.

	
· Patients younger than one year and older than 49 years.

	
This calculator is not intended to replace clinical judgement. The risk of life-threatening arrhythmic events should be interpreted as a continuum in the context of the patient’s clinical condition.